NERVE HEARING LOSS



The structures involved in a nerve hearing loss (otherwise called ‘sensorineural’ or ‘perceptive’)  include the cochlea and eighth cranial nerve, are locked away inside the bones at the bottom of the skull. The sounds of language are coded in high frequencies and in the low frequencies. When normal hearing people have difficulty hearing speech sounds in the low frequencies, they figure them out from what they hear in the high frequencies. In a noisy background, we count on both. 

In addition to affecting the loudness of hearing, nerve hearing loss produces distortion of the sounds entering the ear. Someone with this kind of loss  may be aware of sounds, but makes errors deciding exactly what sounds represent. People with a nerve hearing loss
experience difficulty  decoding the complicated sounds we string together to make speech. 

In noisy situations, people with a nerve hearing loss - which almost always affects the high frequencies first -  have the greatest difficulty.

Until recently, most of these losses were attributed to "old age". We are now wiser and understand that the tendency to develop these losses probably runs in families and is aggravated by the noise pollution in our society. In fact, the gene for bringing this hearing
loss may be located on the chromosome very near the gene for longevity, thus explaining why older people so often have this type of hearing loss.  A preventable cause of such loss is work exposure to loud  noises. Certain medications, occasionally required in the treatment of life-threatening infections , have been found to damage the hearing nerve.

The person who has this hearing loss usually doesn't know  it.  The damage usually occurs gradually and since we usually don't know what is going to be said to us, we can only accept what our ears tell us as the truth.  When hearing deteriorates to a moderately  severe
level we finally become aware what our ears are telling us can’t possibly be correct.  People  who have normal hearing and who know what they and others are saying know that the person with sensori-neural loss has lost hearing before they do.

People with a nerve loss have problems communicating with friends and family.  Though they hear what is being said, they often hear it incorrectly and having a conversation becomes very difficult. Often, families give up trying to get through to the person who has a nerve loss.  It is a rare friend who continues to try.  For the person with a nerve hearing loss, a public gathering such as a party or a performance is a disaster. Often the person with a nerve hearing loss begins to avoid going into public without realizing why. The telephone becomes a major source of communications, since it is easier to understand on the telephone than face-to-face at an moderate stage of deterioration. This explains why so many of our senior citizens spend so much time on the telephone speaking to people whom they could probably just as easily visit face-to-face.

Through the next few decades, we don't foresee any readily available surgical or medical treatment for most nerve hearing losses. The best ways to improve communications include: